presentamos un caso de displasia fibrosa monostótica localizada en el seno entre ellos el síndrome de albright (sólo en casos de displasia poliostótica). su. Displasia fibrosa monostótica e poliostótica. Front Cover. Simone Paula Bibliographic information. QR code for Displasia fibrosa monostótica e poliostótica. Download PDF. 1 / 3 Pages. Previous article. Go back to website. Next article.

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In the present case, the patient reported no pain, except a very mild intra-oral deformity without aesthetic or functional impairment.

The patient did not remember to have suffered any trauma on the region. Fibrous dysplasia is a benign fibrous-osseous lesion in which normal bone is replaced by fibrous connective tissue and immature bone, affecting only one monostotic or several bones polyostotic and mainly occurring in children and young adults.

Alves 1Fernando Canavarros 2Daniela S.

Fibrous dysplasia FD is a non-neoplastic benign disorder in which normal bone is replaced by fibrous tissue and immature bone 1812 – 1620 – 21which may affect one monostotic or more bones polyostotic 1417 Conservative treatment is usually based on treating asymptomatic cases of FD 6.

Clinically, FD can be classified as monostotic when limited to only one bone and polyostotic when more bones are involved 1 – 25 – Imaging of craniofacial fibrous dysplasia. Implant radiography and radiology.

The polyostotic form is rarer and mainly occurring in long bones 610 and possibly associated with McCune-Albright syndrome, which is characterised by the presence of coffee-milk cutaneous pigmentation and endocrinopathy 136 – 1016 According to Akintoye et al.

World J Surg Oncol. Reversible visual loss caused by fibrous dysplasia. It is worth emphasising that the initial lesions are more radiolucent, becoming more radiopaque as the lesion develops 16 FD is a rare but potentially severe disease which can cause fracture when affecting long bones, including osseous pain, deformities and compression of surrounding tissues 17. McCune Albright syndrome – diffuse orbital involvement due to fibrous dysplasia: Rev Cir Traumatol Buco-Maxilo-fac.


Maxilla and mandible are the most affected bones in the craniofacial region 11with the lesion affecting more commonly the posterior than the anterior regions of the arch 2 and being more frequent in the buccal region CBCT image revealed a slight facial asymmetry, whereas intra-oral examination showed an increased bone volume in the buccal region, normal sound fibrous mucosa, prolonged retention of tooth 63 and presence of orthodontic wire for traction of partially-impacted tooth According to Lisle et al.

Displasia fibrosa poliostótica: presentación de un caso

The main differential didplasia of the monostotic form on head and neck bones is Ossifying Fibroma which some consider another form of the same entity. Although some studies reported the indication of magnetic resonance imaging MRI for diagnosis of Monlstotica 62026this type of examination does not fiibrosa the distinctive characteristic of FD as observed in radiographs and CT images 6820since the lesion may often be confounded with tumours 68.

CBCT has provided important clinical contribution by allowing us to evaluate lesions in detail and the precise involvement of surrounding tissues, including pre-surgical evaluation when necessary and follow-up of the patients. Craniofacial fibrous dysplasia CFD of the maxilla in an year old boy: Primary bone tumors of the orbit.

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In the panoramic, axial, coronal and three-dimensional reconstructions Figures 1 to 4 one can observe the image of a heterogeneous, expansive, bone density with irregular contour and unpolished glass appearance involving the alveolar ridge, extending from the incisor region to the second upper left molar, displacement of teeth 21 and 23, changes in the lamina dura and periodontal ligament, but without root resorption. We report a rare jonostotica of McCune Albright syndrome in a boy, who presented bilateral and diffuse involvement of orbits but few external craniofacial distortions.

The purpose of this study is to make a review of the main clinical, radiological and histopathological findings that contributes to the differential diagnosis.

Moreover, neurological symptoms such as headache, poor visual acuity, diplopia, paresthesia 1 – 2816 – 1720 – 21nasal obstruction 21621hearing loss 21720 and sinusitis-like symptoms 2 can occur when craniofacial bones are affected. Due to the unpolished glass appearance of FD on the images 13the imaging diagnosis is enough and thus bone biopsy is not necessary 8 Unilateral blindness after ipsilateral prophylactic transcranial optic canal decompression for fibrous dysplasia.


Br J OralMaxillofac Surg.

In addition, because the patient was 10 years old, a follow-up by means of imaging examinations to be performed periodically was proposed in order to avoid possible relapse in the case of surgical treatment.

Ossifying fibroma involving the paranasal sinuses, orbit, and anterior cranial fossa: However, in the majority of the cases, the unpolished glass appearance was the most prevalent image 8 En bloc resection and bone graft: Craniofacial and monostotic variants of fibrous dysplasia affecting themaxillofacial.

Fibrous dysplasia FD is a rare benign fibro-osseous lesion 1 – 7 characterised by the gradual replacement of the normal bone by fibrous tissue and immature bone 58. All of them had recurrences after surgical removal, diagnosed between first and eighth year of follow up. Multiplanar reconstructions MPR and 3D volume images were obtained. As the majority of the monostotic lesions are asymptomatic, they are only discovered by means of imaging examinations ordered for other purposes 13 All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License.

One can also observe that the mucosa covering the affected bone appears to be healthy and normal 10 The increased familiarity with the imaging characteristics of fibrous dysplasia can assist the dentist-surgeon in the early diagnosis and treatment of patients. Accuracy of linear measurements of Galileos cone beam computed tomography in normal and different head positions.

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